Реферат: Ангиология в детской хирургии
ÄÂÃÌÓ
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<span Park Avenue",«serif»; font-weight:normal">Êàôåäðà
<span Park Avenue",«serif»;font-weight:normal"> äåòñêîé õèðóðãèè<span Park Avenue",«serif»; font-weight:normal">Çàâ
<span Park Avenue",«serif»;font-weight:normal">. êàô. Í.Ã. Æèëà, äîöåíò<span Park Avenue",«serif»; font-weight:normal">Àññèñòåíò
<span Park Avenue",«serif»;font-weight:normal">: Þ.À. Êðàâöîâ<span Park Avenue",«serif»; font-weight:normal">
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ÄÅÒÑÊÎÉ
ÕÈÐÓÐÃÈÈ
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607 ï.ô.
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<span Park Avenue",«serif»">Àíãèîëîãèÿ
<span Park Avenue",«serif»"> âäåòñêîé õèðóðãèè<span Park Avenue",«serif»;mso-ansi-language: X-NONE">
<span Park Avenue",«serif»">Âðîæäåííûå
<span Park Avenue",«serif»"> çàáîëåâàíèÿñîñóäîâ ó äåòåéçà÷àñòóþïîïàäàþòâ ïîëåçðåíèÿ äåòñêèõ õèðóðãîâ. Îáùèì òåðìèíîì“ñîñóäèñòàÿäèñïëàçèÿ”îáúåäèíÿþòñÿíàèáîëåå÷àñòî âñòðå÷àþùèåñÿ âèäû ñîñóäèñòûõçàáîëåâàíèé:<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
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<span Park Avenue",«serif»;mso-ansi-language:X-NONE">èñòèííûå<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ïîðîêè ðàçâèòèÿ;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ãåìàíãèîìû<span Park Avenue",«serif»;mso-ansi-language:X-NONE">;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">êèñòû<span Park Avenue",«serif»;mso-ansi-language:X-NONE">;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ñîñóäèñòûå<span Park Avenue",«serif»;mso-ansi-language:X-NONE">îïóõîëè.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Äîáðîêà
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">÷åñòâåííûåè çëîêà÷åñòâåííûåäèñïëàçèèìîãóò ïðîèñõîäèòüèç åäèíîéòêàíè, ðàçíÿñü ïî òå÷åíèþ.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ê äèñïëàçèÿìîòíåñåíûè òàêèåäèñïðîïîðöèèðàçâèòèÿñîñóäîâ, ïðè êîòîðûõ,íàïðèìåð,îòìå÷åííîåó íîâîðîæäåííîãîàíãèîìàòîçíîåïîðàæåíèåïîâåðãàåòñÿñàìîïðîèçâîëüíîìóèçëå÷åíèþ.
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<span Park Avenue",«serif»; mso-ansi-language:X-NONE">Ïîäðàçäåëåíèÿ
<span Park Avenue",«serif»; mso-ansi-language:X-NONE"> ñîñóäèñòûõäèñïëàçèé:<span Park Avenue",«serif»;mso-ansi-language: X-NONE">
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<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ïî<span Park Avenue",«serif»;mso-ansi-language:X-NONE">èñòî÷íèêó.Ëèìôàòè÷åñêèåñîñóäû(ËÄ), âåíû(ÂÄ), àðòåðèèè êàïèëëÿðû(ÀÄ).¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ïî<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ñî÷åòàíèþ.Îäíà-äâå-òðè ñìåøàííûå(ñ íåñîñóäèñòûìè).¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ïî<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ðàñïðîñòðàíåíèþ.Îäèíî÷íûå,ìíîæåñòâåííûå.¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ïî<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ïàòîìîðôîëîãè÷åñêîìó ñòðîåíèþ.Àãåíåçèÿ,ãèïîïëàçèÿñîñóäà, àíåâðèçìà,áëîêàäà ñòâîëà èëè ëèìôîóçëà,äåôåêòû êëàïàíîâ ñòâîëà èëè ëèìôîóçëà,ôèñòóëû.¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ïî<span Park Avenue",«serif»;mso-ansi-language:X-NONE">òå÷åíèþ.Ðåãðåññèðóþùèå,ïðîãðåññèðóþùèå,ñòàáèëüíûå.¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ïî<span Park Avenue",«serif»;mso-ansi-language:X-NONE">êëèíè÷åñêèìïðîÿâëåíèÿì(ìåñòíûå,îòäàëåííûå).<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ëèìôàòè÷åñêèå
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">äèñïëàçèè(ËÄ) ÿâëÿþòññÿêèñòàìè,ðàñòóùèìèçà ñ÷åòýíäîòåëèÿè êàïèëëÿðîâè íàïîëíåíûëèìôîé.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ëîêàëèçàöèÿ
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">è õàðàêòåðñîîòâåòñâóåòýìáðèîãåíåçóïåðâè÷íûå ëèìôàòè÷åñêèåìåøêè – ÿðåìíûå, ïîäêëþ÷è÷íûå, çàáðþøèííûå,ïîäâçäîøíî-ïîÿñíè÷íûå,ïîäâçäîøíî-ïàõîâûåè çîíûñêîïëåíèÿëèìôîóçëîâ. êëèíèêåíàáëþäàþòñÿïîðàæåíèÿñ ìîìåíòàðîæäåíèÿðåáåíêà èëè ïîÿâëÿþùèåñÿïîçäíåå.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Çíà÷àíèÿ
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">â õàðàêòåðåçàáîëåâàíèéèìåþò áëîêàäà ëèìôîóçëà,íåïðàâèëüíàÿçàêëàäêàëèìôàòè÷åñêèõïóòåé, ýêòàçèÿ èëè ñîîáùåíèåñ âåíîçíîéñèñòåìîé.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Êðóïíûå
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">êèñòû (ãèãðîìû) ìîãóò çàòðóäíÿòüäûõàíèå.Ðàñïðîñòðàíÿÿñüíà ïåðåäíþþïîâåðõíîñòüïîçâîíî÷íèêà,ïèùåâàäà,òðàõåè, â ïîäêëþ÷è÷íóþîáëàñòü è ïîäúÿçû÷íîåïðîñòðàíñòâî,îíè ñîñçäàþòîïàñíóþ äëÿ æèçíèñèòóàöèþ.Ó íîâîðîæäåííûõíàáëþäàåòñÿõèëîòîðàêñè õèëîïåðèòîíåóìþ<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Êèñòû
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">,ðàñïîëîæåííûåâ çàáðþøèííîìïðîñòðàíñòâå,ñïóñêàÿñüâ ìîøîíêó,ñèìóëèðóþòãðûæó, à ïîäíèìàÿñüâ ïîÿñíè÷íóþ îáëàñòü,ìîãóò ïðîðûâàòüñÿâ áðþøíóþïîëîñòü, äåëàÿ êàðòèíóîñòðîãî æèâîòà.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Àãåíåçèÿ
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ëèìôàòè÷åñêèõïóòåé èëè áëîêàäàèõ â ëèìôîóçëàõ,äàåò êàðòèíóëèìôåäåìû. ïðîöåññðàíî âîâëåêàþòñÿïîäêîæíî-æèðîâàÿ êëåò÷àòêàè êîæà.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE"> êèøå÷íèêåËÄ ïðîÿâëÿåòñÿêëèíèêà ýíòåðîïàòèè.
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<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Áëàñòîìàòîçíûé
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">,çëîêà÷åñòâåííûéðîñò (ëèìôîñàðêîìû)íàáëþäàåòñÿ÷àùå âñåãîâ çàáðþøèííîéêëåò÷àòêå.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Òàêòèêà
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ëå÷åíèÿËÄ îïðåäåëÿåòñÿåå âèäàìè,ëîêàëèçàöèåé,íàðóøåíèåìôóíêöèé è äð. Íåîòëîæíîåâìåøàòåëüñòâî(ïóíêöèþ èëè îïåðàöèþ)ïðîèçâîäÿòó íîâîðîæäåííûõñ çàòðóäíåíèÿìèäûõàíèÿ èëè ïðèñèìïòîìàõîñòðîãî æèâîòà. Äðåíàæè óäàëàþò íå ðàíåå,÷åì íà6-10 ñóòêè, èáî ðåöèäèâèðîâàíèåñêîïëåíèÿëèìôû â ðàíåòðåáóåò åå ïîâòîðíîãîäðåíèðîâàíèÿ.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ïðè
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ñëîíîâîñòèðàííåå êîíñåðâàòèâíîåëå÷åíèå ó ãðóäíûõäåòåé â ïîñëåäíèåãîäû ñî÷åòàþò ñîïåðàöèÿìè.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Âåíîçíûå
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">äèñïëàçèè(ÂÄ) ñîçäàþòðàçíîîáðàçíóþêëèíè÷åñêóþ êàðòèíó.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Âåíîçíàÿ
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">àíåâðèçìàáîëüøîé âåíû Ãîëåíàâ ìîçãå– îäíà èçïðè÷èíãèäðîöåôàëèèè êðîâîèçëèÿíèÿ.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Ïðîãðåññèðóþùàÿ
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ýêòîçèÿ îäíîé èëèäâóõ ÿðåìíûõâåí òðåáóåòèññå÷åíèÿèëè õèðóðãè÷åñêîãî óêðåïëåíèÿ.Íàðóøåíèåâåíîçíîãîîòòîêà îáóñëàâëèâàåòïðîãðåññèðóþùèåïàòîëîãè÷åñêèåèçìåíåíèÿ– òêàíåâûåïðîöåññûòèïà ôèáðîçàè ïàòîëîãè÷åñêèåèçìåíåíèÿâ îðãàíàõè ñèñòåìàõ,ñòðàäàþùèõîò âåíîçíîéãèïåðòåíçèè.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Çìååâèäíî
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">è ÷åòêîîáðàçíîðàñøèðåííûåâåíû ñåìåííîãîêàíàòèÿêà(âàðèêîöåëå)âîçíèêàþòïðè íàðóøåíèèâåíîçíîãîîòòîêà, ñîïðîâîæäàþòñÿíàðóøåíèåìôåðòèëüíîñòè.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ÊÂÄ îòíîñÿòñÿôëåáýêòîçèÿíèæíèõ êîíå÷íîñòåé.Ðàñøèðåíèåâåí ÷àùåíàáëþäàåòñÿíà îãðàíè÷åííîì ó÷àñòêå.
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">Íåñòàáèëüíûå
<span Park Avenue",«serif»;mso-ansi-language:X-NONE">ïîðàæåíèÿ,“èñ÷åçàþùèå”ñîñóäèñòûåîáðàçîâàíèÿ.<span Park Avenue",«serif»;mso-ansi-language:X-NONE">
<span Park Avenue",«serif»">Àðòåðèàëüíûå<span Park Avenue",«serif»"> äèñïëàçèè:<span Park Avenue",«serif»">
<span Park Avenue",«serif»">Ãåìàíãèîìû
<span Park Avenue",«serif»"> – ïîðàæåíèÿðàçëè÷íûõòêàíåéè îðãàíîâãèñòîëîãè÷åñêèñõîäíûìè,êàïèëëÿðîïîäîáíûìèñîñóäèñòûìèðàçðàñòàíèÿìè.<span Park Avenue",«serif»;mso-no-proof:yes">
<span Park Avenue",«serif»;mso-no-proof:yes">60-70%ðåãðåññèðóåò,15-20% îñòàþòñÿñòàáèëüíûìè,10-25% — ðåñòóò. ÃÀïðîèñõîäÿòèç âñåõ òðåõñëîåâ ñîñóäèñòîéñòåíêè.
<span Park Avenue",«serif»;mso-no-proof:yes">
<span Park Avenue",«serif»;mso-no-proof:yes">Òî÷å÷íàÿÃÀ –òåëåàíãèýêòàçèÿ– ÿðêî-êðàñíàÿïÿòíî 0.5-2 ìì., îòêîòîðîãîðàñõîäÿòñÿâíóòðèêîæíûåñîñóäû.
<span Park Avenue",«serif»;mso-no-proof:yes">
<span Park Avenue",«serif»;mso-no-proof:yes">ÏëîñêàÿÃÀ îêðàøåíàâ êðàñíûéöâåò,äèàìåòð 1-5 ñì.
<span Park Avenue",«serif»;mso-no-proof:yes">
<span Park Avenue",«serif»;mso-no-proof:yes">ÊàïèëëÿðíàÿÃÀ – áîëååÿðêàÿ ïîîêðàñêå, âûñòóïàåòíàäïîâåðõíîñòüþêîæè.
<span Park Avenue",«serif»;mso-no-proof:yes">
<span Park Avenue",«serif»;mso-no-proof:yes">ÊàâåðíîçíûåÃÀ –çàíèìàþòáîëüøóþïëîùàäü,áûñòðî èàãðåññèâíîðàñòóò,äåôîðìèðóþòîðãàíû.
<span Park Avenue",«serif»;mso-no-proof:yes">
<span Park Avenue",«serif»;mso-no-proof: yes">Ëå÷åáíûåïðèåìû ïðè ÃÀ<span Park Avenue",«serif»;mso-no-proof: yes">
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<span Park Avenue",«serif»;mso-no-proof:yes">Áëèçêîôîêóñíàÿðåíòãåíîòåðàïèÿ;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">Îäíîèìíîãîýòàïíàÿõèðóðãè÷åñêàÿýêñòèðïàöèÿñïðåäâàðèòåëüíîéïåðåâÿçêîéèëèýìáîëèçàöèåéñòâîëà èïîñëåäóþùèìçàìåùåíèåìäåôåêòàêîæíûìëîñêóòîì;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">Ìíîæåñòâåííîåïîâòîðíîåïðîøèâàíèåîïóõîëè;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">Ýëåêòðî-,òåðìîêîàãóëÿöèÿ;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">Êðèîòåðàïèÿ;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">Îáëó÷åíèåëàçåðîì;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">Èíúåêöèèñêëåðîçèðóþùèõñðåäñòâ.<span Park Avenue",«serif»;mso-no-proof:yes">
<span Park Avenue",«serif»;mso-no-proof:yes">Çëîêà÷åñòâåííûåÃÀïðåäñòàâëåíûòðåìÿ ñëîÿìèñîñóäèñòîéñòåíêè:
<span Park Avenue",«serif»;mso-no-proof:yes">
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<span Park Avenue",«serif»;mso-no-proof:yes">çëîêà÷åñòâåííàÿãåìàíãèîýíäîòåëèîìà;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">àíãèîëèìôîñàðêîìà;¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">ãåìàíãèîïåðèöèòîìà.<span Park Avenue",«serif»;mso-no-proof:yes">
<span Park Avenue",«serif»;mso-no-proof: yes">Ñèíäðîìûñîñóäèñòîéäèñïëàçèèäëÿ<span Park Avenue",«serif»;mso-no-proof: yes">äèôôåðåíöèàëüíîéäèàãíîñòèêè
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<span Park Avenue",«serif»;mso-no-proof:yes">ÑèíäðîìØòóðãëü-Âåáåðà.Ñî÷åòàíèåïëîñêîãîñîñóäèñòîãîïÿòíà íàëèöå,ñîîòâåòñòâåííîèííåðâàöèèòðîèíè÷íîãîíåðâà èëèëèöåâîãî ñãëàóêîìîé èâíóòðèìûøå÷íîéêàëüöèôèêàöèåé,êàêñëåäñòâèåìèêðîèíôàðêòîâ.¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">ÑèíäðîìËóè-Áàð.Ãåìàíãèîýêòàçèèíà êîíüþêòèâåáëèæå êâåêàì, ïÿòíàíà ëèöå,ðàññòðîéñòâîðàâíîâåíèÿ(àòðîôèÿ ìîçæå÷êà).¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">ÑèíäðîìÃåâåíàðà.Ðàñïàäàþùèåñÿÿçâû íà ñòîïàõíîâîðîæäåííûõ,íàïîìèíàþùèåäèàáåòè÷åñêèåè äðóãèåãàíãðåíû –ñëåñäñòâèåêîíöåâûõâåòâåéàðòåðèè.¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">ÑèíäðîìÊàçàáàõà-Ìåðèòòà.Îáøèðíûåêàâåðíîçíûåñîñóäèñòûåïîðàæåíèÿ.Êðîâîòî÷èâîñòüñâÿçàíà ñáûñòðîíàðàñòàþùåéòðîìáîöèòî-ïåíè÷åñêîéïóðïóðîé,ìîæåòïîñëóæèòüïðè÷èíîéãèáåëè.¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">ÑèíäðîìÊëåïïåëÿ-Òðåíîíå.Óâåëè÷åíèåðàçìåðîâêîíå÷íîñòè,ðàñøèðåíèåïîäêîæíûõ âåííèæíåéêîíå÷íîñòè.Ïðè÷èíîéáûâàåò ïðåïÿòñòâèåîòòîêó ïî ãëóáîêèìâåíàìè(àíîìàëüíûåàðòåðèàëüíûåñòâîëû,àïëàçèÿ èãèïîïëàçèÿãëóáîêèõ âåí,òÿæèðóáöîâîé èñóõîæèëüíîéòêàíè). Ïëîñêèåàíãåîìûäîïîëíÿþòêàðòèíó.¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">ÑèíäðîìÏàðêñà-Âåáåðà.Íàëè÷èåêðóïíûõ àðòåðèîâåíîçíûõôèñòóë èàíåâðèçì.¨<span Times New Roman"">
<span Park Avenue",«serif»;mso-no-proof:yes">ÑèíäðîìÒåðëåðà,ïðîÿâëÿþùèéñÿóíîâîðîæäåííûõëèìôåäåìîéêîí÷íîñòåéâ ðåçóëüòàòåâðåìåííîéâðîæäåííîé íåäîñòàòî÷íîñòèëèìôàòè÷åñêèõêëàïàíîâ.Ïðèâëåêàåòâíèìàíèåêðûëîâèäíàÿøåÿ.<span Park Avenue",«serif»;mso-no-proof:yes">Ïðèîáñëåäîâàíèè:àïëàçèÿÿè÷íèêîâ,êîàðêòàöèÿàîðòû,áðàõèäàêòèëèÿ,çàäåðæêà ðîñòà.
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<span Park Avenue",«serif»;mso-no-proof:yes">Âîòëè÷èå îòâçðîñëûõ ÑÄ âïåðâûå ãîäûæèçíèðåáåíêàíåðåäêîïîäâåðãàþòñÿáûñòðûìïðåîáðàçîâàíèÿì(áóðíîìóðîñòó,îáðàòíîìóðàçâèòèþ).Ýòî ÿâëÿåòñÿîñíîâàíèåìâûäåëåíèÿêëèíè÷åñêîéïåäèàòåðè÷åñêîéàíãèîëîãèè.
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<span Park Avenue",«serif»;mso-no-proof:yes">Ëèòåðàòóðà:
<span Park Avenue",«serif»;mso-no-proof:yes"><span Park Avenue",«serif»; mso-no-proof:yes">
<span Park Avenue",«serif»; mso-no-proof:yes">Æóðíàë“Õèðóðãèÿ”, ¹5,6,1992ã.
<span Park Avenue",«serif»; mso-no-proof:yes">Àâòîð: Ñ.ß.Äîëåöêèé,÷ëåí-êîðð.ÀÌÍ(ã.Ìîñêâà)
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